AntibodiesCollagen VI Antibody

PDF

251203

0.1 mg

Brand

Abbiotec

Description

Collagen VI acts as a cell-binding protein. Collagen VI is a trimer composed of three different chains: alpha-1(VI), alpha-2(VI), and alpha-3(VI) or alpha-5(VI) or alpha-6(VI). Defects in collagen VI are a cause of Bethlem myopathy (BM). BM is a rare autosomal dominant proximal myopathy characterized by early childhood onset (complete penetrance by the age of 5) and joint contractures most frequently affecting the elbows and ankles.

Application

ELISAIHC

Reactivity

BCanineChickenHumanMouse

Photos

  • Collagen VI Antibody